Abstract

Neuromuscular diseases (NMDs) comprise a heterogeneous group of conditions characterized by extreme progressive muscle weakness leading to respiratory failure. Noninvasive mechanical ventilation (NIV) has emerged as a cornerstone in the management of respiratory complications associated with NMDs. This review aims to elucidate the role of NMV in respiratory function, improving quality of life, and prolonging survival in individuals with NMD. The physiological basis of respiratory impairment in NMDs, principles of NMV application, evidence supporting its efficacy, patient selection criteria, and potential challenges in its application are discussed.

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Authors

Paolo Banfi - IRCCS Fondazione Don Carlo Gnocchi – ONLUS, Milan, Italy https://orcid.org/0000-0001-8162-0751

Agata Alba Maria Domenica Buscemi - espiratory Unit and Cystic Fibrosis Center, Fondazione IRCCS Cà Granda Ospedale Maggiore Policlinico, Milano, Italy; Department of Pathophysiology and Transplantation, Università degli Studi di Milano, Italy https://orcid.org/0000-0002-4742-392X

Elena Compalati - IRCCS Fondazione Don Carlo Gnocchi – ONLUS, Milan, Italy https://orcid.org/0000-0001-7439-184X

Martina Pisoni - IRCCS Fondazione Don Carlo Gnocchi – ONLUS, Milan, Italy

Marco Mantero - espiratory Unit and Cystic Fibrosis Center, Fondazione IRCCS Cà Granda Ospedale Maggiore Policlinico, Milano, Italy; Department of Pathophysiology and Transplantation, Università degli Studi di Milano, Italy https://orcid.org/0000-0001-7324-1217

Agata Lax - IRCCS Fondazione Don Carlo Gnocchi – ONLUS, Milan, Italy https://orcid.org/0000-0002-5928-3485

How to Cite
Banfi, P., Buscemi, A. A. M. D. ., Compalati, E., Pisoni, M., Mantero, M. ., & Lax, A. (2024). Enhancing respiratory function in neuromuscular disease: the role of non-invasive ventilation. A narrative review. Acta Myologica, 43(2). https://doi.org/10.36185/2532-1900-506
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